Developmental venous anomaly

  • Congenital cerebral vascular malformation with mature venous elements
  • Umbrella-like collection of enlarged medullary (white matter) veins ("Medusa head")
  • At angle of ventricle
  • Converge on single enlarged collector vein
  • Imaging
    • CT often normal but may see hyperdense collector vein
    • MR
      • Hypointense on SWI
      • Strong enhancement
      • T1 can be normal if small and signal is variable depending on size and flow (eg. flow void may or may not be present)
      • T2 tubular flow void present
      • FLAIR usually normal but occasionally will see hyperintensity adject which reflects venous congestion/ischemia
      • Best imaging is T1 w/ contrast which shows strong enhancement
  • Can be mixed with cavernous malformations (mixed vascular malformation) with coexisting cavernous and or capillary malformations occurring 15-20% of the time
  • More common asymptomatic
  • 0.15% risk of hemorrhage per lesion per year
  • Solitary DVAs usually not treated as attempts can lead to venous infarction
  • If mixed then treatment depends on the mixed component
  • Per CTC it is a "do not touch" lesion. If resected can lead to debilitating venous infarct similar to acute thrombosis of DVA. DVA must be preserved if an adjacent cavernous malformation is resected