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Interstitial lung disease

UIP

  • Does not respond to treatment the same way other ILDs do, needs a different treatment
  • Classic hallmarks: honeycombing, peripheral distribution (ie. touching the pleura), and very low DLCO
  • Pathology is NOT the gold standard for diagnosis, imaging is
    • Fleischner 2017 whitepaper recommends reporting findings as “typical”, “probable”, or “indeterminate/consistent with another dx”
  • Always search for nodule (given increased cancer risk), pulmonary HTN, and new ground glass (which may represent rapidly active disease)